2023 HiHASC共识指南:成人疑似噬血细胞性淋巴组织增生症的诊断和调查

2024-01-06 Lancet Rheumatol 发表于上海

本文主要针对人疑似噬血细胞性淋巴组织增生症的诊断和调查提供共识指导,重点是早期识别和诊断HLH,并同时确定根本原因。

中文标题:

2023 HiHASC共识指南:成人疑似噬血细胞性淋巴组织增生症的诊断和调查

英文标题:

Diagnosis and investigation of suspected haemophagocytic lymphohistiocytosis in adults: 2023 Hyperinflammation and HLH Across Speciality Collaboration (HiHASC) consensus guideline

发布机构:

发布日期:

2024-01-06

简要介绍:

噬血细胞性淋巴组织增生症(HLH)是一种以细胞毒性淋巴细胞和巨噬细胞持续活化为特征的高炎症综合征,如果不治疗,可导致多器官功能障碍和死亡。本文主要针对人疑似噬血细胞性淋巴组织增生症的诊断和调查提供共识指导,重点是早期识别和诊断HLH,并同时确定根本原因。

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